Overview

What is Ebstein's anomaly in adults?

Ebstein's anomaly is a rare congenital cardiac defect. Congenital refers to something present at birth. Anything unexpected or unusual is termed an anomaly. The tricuspid valve, one of four valves in your heart, is affected by Ebstein's anomaly. In 1866, German physician Wilhelm Ebstein first described the illness.

What are the symptoms of Ebstein anomaly?

The illness and the condition can be from mild to severe, as characterized by the defect. In some extreme cases, manifestations arise shortly after birth or at an early age. Cyanosis can manifest itself in bluish bruises on the skin due to low levels of oxygenated blood in the system. In some instances, signs of heart failure can be detected prenatally by even including the following conditions:

• Rapid breathing.
• Shortness of breath.
• Failure to gain weight.
• Swelling (edema) in the legs, abdomen, or around the eyes.
• Fast heart rate

What causes Ebstein's anomaly?

The doctor does not know why Ebstein's anomaly occurs. He believes that it is probably a result of hereditary and environmental factors, and he doesn't know his exact cause yet.

How are Ebstein anomalies diagnosed and tested?

A physician will conduct examinations and check your vital signs. You might be subjected to one of the tests listed below to get an idea of how well the heart is working:

• An electrocardiogram (ECG)
• ChestX-ray
• Heart MRI
• Echocardiogram
• Holter monitor

What is the treatment of Ebstein anomaly?

Treatment for an adult Ebstein's anomaly will largely depend on the severity of the disease and the symptoms expressed by the patient. The approaches include monitoring adults with mild Ebstein's anomaly who are asymptomatic and may need to undergo monitoring at irregular intervals through echocardiography. This monitors changes in the anatomy or physiology of the heart.

Medication:

Information such as antiarrhythmic medications could be given if side effects like arrhythmias or irregular pulses persist. Medically, surgery would be an option if symptoms continue to improve, and cardiogenic shock or increased difficulty occurs. Surgery goals include the replacement or repair of the tricuspid valve and the correction of any potential problem that may occur. There are several surgical options:

• Tricuspid valve repair: This is the preferred course of action if practicable. The surgeon repairs the damaged tricuspid valve by doctoring holes, redundant removal of tissue, or reshaping the valve circulars to upgrade its function.
• Tricuspid valve: If repair is impossible, then implantation of a mechanical or natural prosthetic valve has become possible so that the broken valve can be substituted.
• Ancillary procedures: The physicians would correct the other extraneous abnormalities of having an elongated right ventricle or defects in the atrial septum. Atrial septal defects are holes in the walls between the heart's two upper chambers.

What happens to the tricuspid valve in the case of Ebstein's abnormality?

For those patients who have Ebstein's anomaly, the valve is:

• Valve's circulars are moving parts with an unusual shape; they may cleave to the heart wall, and can open up and shut down in response to a pulse.
• Malposition: Usually, it is located lower than it should be.

These defects lead to regurgitation, or flow back, into the heart's right upper chamber right atrium. In addition, the atrium may be hypertrophic and very enlarged. Right-sided heart failure could then result from gradual degeneration of the larger portion of the heart over time.

Who is affected?

Many people with Ebstein's defect have other new heart defects at birth. Among the many individuals affected, one gap in the wall that separates the two upper chambers of the heart occurs in as many as 94. Other left-sided heart defects and other heart valve defects are also often present in patients with Ebstein's defect.

Living With

How soon will I be able to see my doctor?

Report any symptoms to your doctor right away if you have Ebstein's anomaly. You may develop new ones. These may include the following: redness of skin, fluid retained beneath the skin that has dropped, and rapid heart rate.

Why Tender Palm Super-Speciality Hospital for Ebstein anomaly?

Tender Palm Hospital has the most experienced team of Cardiologists, Cardiac Surgeons, and diagnostics with the latest and International standard infection control measures in Lucknow, India. The Cardiac Science Centre team has decades of experience in successfully treating Ebstein Anomaly in adults.

To seek an expert consultation for Ebstein Anomaly in Lucknow, India

Call us at +91-9076972161
Email at care@tenderpalm.com

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