Overview

What is total anomalous pulmonary venous return in a child?

Total anomalous pulmonary venous return (TAPVR) is a congenital heart defect present at birth. It affects the four blood vessels referred to as the pulmonary modes, which carry blood rich in oxygen back to the heart's left side from the lungs. In TAPVR, these modes typically don't connect to the left atrium. Instead, they incorrectly empty into the upper right chamber of the heart, the right atrium. 

The issue with TAPVR in child-

Regular Rotation: Deoxygenated blood is pumped to the lungs by the right ventricle, which in a normal heart comes out of the body from the right patio. In the lungs, oxygen enters into the blood, which in turn becomes oxygen-rich. This oxygen-rich blood travels through the left atrium and left ventricle and the pulmonary pathways before coming out of the body.

Total Anomalous Pulmonary Venous Return (TAPVR dislocation): When TAPVR is used, the oxygen-rich blood from the lungs does not reach the left patio. It empties into the right atrium, where it mixes with oxygen-poor and systematically flows away from the body blood.

  • The amount of oxygenated blood supplied to the body's parts and tissues is decreased because of this mixing of oxygenated and deoxygenated blood.
  • The location of the anomalous connection determines the subtype of TAPVR and the degree to which symptoms are invariable. Sometimes, there can be an additional ostium (atrial septal defect) between the right and left patios that partially admits oxygenated blood into the left atrium.

What are the symptoms of Total anomalous pulmonary venous return in a child?

  • Blue coloring of lips, skin, and nails (cyanosis)
  • Rapid breathing or more effort to breathe, especially while feeding.
  • Heart murmurs are additional heart noises when a doctor listens using a stethoscope.

What causes Total Anomalous Pulmonary Venous Return in a child?

Doctors do not know exactly what triggers total anomalous pulmonary venous return TAPVR. This is caused by an error of your baby's fetal development in the womb. Sometimes, pediatric cardiologists diagnose this defect during the antenatal period through an antenatal echocardiogram, which is highly helpful in preparing. The condition does not appear to be hereditary (passed down within families). However, sometimes siblings are born with the same heart disease.

How do healthcare providers treat total anomalous pulmonary venous return (TAPVR) in a child?

Healthcare providers treat TAPVR through open-heart surgery.

This surgery is generally done as soon as the diagnosis is confirmed. During general anesthesia and while your baby is asleep, a surgeon cuts (makes lacerations) into your baby's chest and heart.

They connect the pulmonary modes to the correct location in your baby's heart. However, the surgeon will also seal the hole, if your baby also has a hole between the left and right atria (atrial septal defects).

What is the diagnosis and test of total anomalous pulmonary venous return (TAPVR) in a child?

Your baby's pediatrician will do a test and listen to your baby's heart. To see a film of your child's heart, they may recommend a chest X-ray. CT (computed tomography) check-up

  • Echocardiogram (echo)
  • Electrocardiogram (EKG or ECG)

These tests allow your baby's doctor to view pictures of the heart and types of your baby. They also assist your baby's provider in making an estimation about blood inflow and finding abnormalities.  

What is the treatment for total anomalous pulmonary venous return (TAPVR) in a child?

In most cases, surgical repair of TAPVR must take place when the child is still an infant. Whether surgery should take place depends on whether there is an obstruction. Surgeons reconstruct the heart by connecting the pulmonary veins to the left upper heart chamber and sealing the hole between the heart's upper chambers.

A person with total anomalous pulmonary venous return needs to be followed throughout life with routine medical exams to monitor for infections, blockages, and problems in cardiac rhythm. A congenital cardiac disorder requires a healthcare provider trained to manage such defects. We call this type of healthcare provider a congenital cardiologist.

Living with 

When should I take my child to the doctor?

  • Get medical help right down
  • If your baby's skin, nails, or lips are blue or gray.
  • Are they having trouble breathing or eating?
  • Appears sleepy.

Why Tender Palm Super-Speciality Hospital for Pediatric Total Anomalous Pulmonary Venous Return?

Tender Palm Hospital has the most experienced team of Pediatric Cardiologists, Pediatric Cardiac Surgeons, and diagnostics with the latest and International standard infection control measures in Lucknow, India. The Pediatric Cardiac Science Centre team has decades of experience in successfully treating Pediatric Total Anomalous Pulmonary Venous Return.

To seek an expert consultation for Pediatric Total Anomalous Pulmonary Venous Return in Lucknow, India

Call us at +91-9076972161
Email at care@tenderpalm.com

Request an Appointment
Mon - Sat 9:00 AM to 6:00 PM IST

Our Experts

Dr. Krishna Kumar Sahani
Dr. Krishna Kumar Sahani
Consultant - Cardiology

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